Faculty Information - MIURA Ken'ichirou

（Last updated : 2026-04-13 15:52:40）

MIURA Ken'ichirou
Department School of Medicine(Tokyo Women's Medical University Hospital), School of Medicine

Position Professor

■ Published papers

1.	Case report	Early-onset kidney failure in a girl with autosomal dominant tubulointerstitial kidney disease due to a de novo UMOD variant. 2026/02
2.	Original article	Annual dialysis data report 2022, Japanese Society for Dialysis Therapy(JSDT) Renal Data Registry 2025/07/01
3.	Case report	Partial bladder transplantation with en bloc kidney transplant-long-term, 17 years, the outcome of a "bladder patch technique" 2024/11
4.	Original article	Protocol for the nationwide registry of patients with polycystic kidney disease: japanese national registry of PKD (JRP) 2024/10
5.	Other	Prediction of 10-yr Renal Graft Survival of Deceased Donors Based on Preoperative Data Using Machine Learning 2024/06
6.	Original article	透析の年次データ報告であるJSDT Renal Data Registry 2020年版(Annual dialysis data report 2020, JSDT renal data registry) 2024/03/11
7.	Original article	A multi-institutional study found a possible role of anti-nephrin antibodies in post-transplant focal segmental glomerulosclerosis recurrence. 2024
8.	Original article	A nationwide survey of MYH9-related disease in Japan 2024
9.	Original article	En bloc kidney transplantation from pediatric donors to teenage recipients: Two case reports. 2023/12/27
10.	Original article	JSDT Renal Data Registryによる年次透析データ報告(2019年版)(Annual dialysis data report 2019, JSDT Renal Data Registry) 2023/09/19
11.	Original article	Medical and psychosocial outcomes in adolescents and young adults with childhood-onset end-stage kidney disease: a multicenter study in Japan 2023/02/18
12.	Original article	Precise clinicopathologic findings for application of genetic testing in pediatric kidney transplant recipients with focal segmental glomerulosclerosis/steroid-resistant nephrotic syndrome. 2023/02
13.	Original article	Depression and health-related quality of life in adolescents and young adults with childhood-onset end-stage kidney disease: a multicenter study in Japan 2023
14.	Original article	Pioglitazone enhances proteinuria reduction in complicated pediatric nephrotic syndrome 2023
15.	Original article	Successful administration of eltrombopag in preparation for peritoneal dialysis catheter placement in a girl with MYH9-related disease. 2023
16.	Review article	Cystic Kidney Diseases That Require a Differential Diagnosis from Autosomal Dominant Polycystic Kidney Disease (ADPKD). 2022/11
17.	Original article	Urinary extracellular vesicles signature for diagnosis of kidney disease 2022/11
18.	Original article	Cumulative dialytic glucose exposure is a risk factor for peritoneal fibrosis and angiogenesis in pediatric patients undergoing peritoneal dialysis using neutral-pH fluids 2022/08
19.	Original article	Circulating nephrin autoantibodies and posttransplant recurrence of primary focal segmental glomerulosclerosis. 2022/04/26
20.	Other	Bickerstaff brainstem encephalitis treated using selective plasma exchange owing to anaphylaxis attributed to fresh frozen plasma: A case report 2022/03
21.	Original article	Safe Renal Transplantation to the Extraperitoneal Cavity in Children Weighing Less Than 15 kg. 2022/03
22.	Original article	A case of Dent disease type 2 with large deletion of OCRL diagnosed after close examination of a school urinary test 2022/01/31
23.	Original article	Acute kidney injury due to ammonium acid urate stones in a patient with adenovirus gastroenteritis: a case report 2022
24.	Original article	Response to steroid and immunosuppressive therapies may predict post-transplant recurrence of steroid- resistant nephrotic syndrome 2022
25.	Original article	A case of early onset cystinuria in a 4-month-old girl 2021/10/20
26.	Other	Committee of Clinical Practical Guideline for Polycystic Kidney Disease 2020. A digest from evidence-based Clinical Practice Guideline for Polycystic Kidney Disease 2020 2021/09/26
27.	Case report	Analysis of water and electrolyte imbalance in a patient with adipsic hypernatremia associated with subfornical organ-targeting antibody. 2021/08
28.	Other	Peritoneal Dialysis Guidelines 2019 Part 1 (Position paper of Japanese Society of Dialysis Therapy) 2021/07/18
29.	Other	Peritoneal Dialysis Guidelines 2019 Part 1 (Position paper of Japanese Society of Dialysis Therapy) 2021/07/13
30.	Original article	Degree of foot process effacement in patients with genetic focal segmental glomerulosclerosis: a single-center analysis and review of the literature 2021/07/08
31.	Original article	Response to steroid and immunosuppressive therapies may predict post-transplant recurrence of steroid-resistant nephrotic syndrome 2021/06
32.	Original article	Clinical and histological features in pediatric and adolescent/young adult patients with renal disease; a cross-sectional analysis of the Japan Renal Biopsy Registry(J-RBR) 2021/05/28
33.	Original article	Kidney biopsy guidebook 2020 in Japan. 2021/04
34.	Original article	Laminin β2 variants associated with isolated nephropathy that impact matrix regulation. 2021/03/22
35.	Original article	Amount and selectivity of proteinuria may predict the treatment response in post-transplant recurrence of focal segmental glomerulosclerosis: a single-center retrospective study. 2021/02
36.	Original article	Any modality of renal replacement therapy can be a treatment option for Joubert syndrome. 2021/01
37.	Case report	Chronic active antibody-mediated rejection with linear IgG deposition on glomerular capillaries in a kidney transplant recipient. 2021/01
38.	Original article	Valganciclovir prophylaxis for cytomegalovirus infection in pediatric kidney transplant recipients: a single-center experience. 2021/01
39.	Original article	Cancer After Pediatric Kidney Transplantation: A Long-term Single-center Experience in JapanTransplantation Direct 2021
40.	Case report	Bardet-Biedl Syndrome Caused by Skipping of SCLT1 Complicated by Microvesicular Steatohepatitis. 2020/11
41.	Original article	Bardet–Biedl syndrome in two unrelated patients with identical compound heterozygous SCLT1 mutations 2020/08/09
42.	Original article	Pathological findings of initial-phase postrenal acute kidney injury 2020/07/03
43.	Case report	Rapid progression to end-stage renal disease in a child with IgA-dominant infection-related glomerulonephritis associated with parvovirus B19. 2020/07
44.	Original article	Development of an exon skipping therapy for X-linked Alport syndrome with truncating variants in COL4A5 2020/06/02
45.	Original article	A nationwide survey on clinical practice patterns and bleeding complications of percutaneous native kidney biopsy in Japan. 2020/05
46.	Original article	Clinical and genetic characterization of nephropathy in patients with nail-patella syndrome. 2020/05
47.	Original article	Incomplete cryptic splicing by an intronic mutation of OCRL in patients with partial phenotypes of Lowe syndrome. 2020/05
48.	Original article	Individualized concept for the treatment of autosomal recessive polycystic kidney disease with end-stage renal disease. 2020/05
49.	Original article	Renal hypoplasia can be the cause of membranous nephropathy-like lesions. 2020/05
50.	Original article	Bardet-Biedl syndrome in two unrelated patients with identical compound heterozygous SCLT1 mutations. 2020/04
51.	Original article	Nonosmotic secretion of arginine vasopressin and salt loss in hyponatremia in Kawasaki disease. 2020/03
52.	Original article	Kidney function of Japanese children undergoing kidney transplant with preemptive therapy for cytomegalovirus infection. 2020/02
53.	Original article	Validation of the Japanese Transition Readiness Assessment Questionnaire. 2020/02
54.	Original article	Deletion in the Cobalamin Synthetase W Domain-Containing Protein 1 Gene Is associated with Congenital Anomalies of the Kidney and Urinary Tract 2020/01
55.	Original article	Long-term outcome of renal transplantation in childhood-onset anti-neutrophil cytoplasmic antibody-associated vasculitis. 2020/01
56.	Review article	A case to use “salt‐losing tubulopathy” instead of “Bartter/Gitelman syndrome” 2020
57.	Original article	Bardet-Biedl Syndrome Caused by Skipping of SCLT1 Complicated by Microvesicular Steatohepatitis. 2020
58.	Original article	Nonosmotic secretion of ADH and salt loss in hyponatremia in Kawasaki disease. 2020
59.	Original article	Validation of the Japanese Transition Readiness Assessment Questionnaire (TRAQ) 2020
60.	Original article	Novel CFHR2-CFHR1 Hybrid in C3 Glomerulopathy Identified by Genomic Structural Variation Analysis 2019/12/01
61.	Original article	Clinical characteristics of HNF1B-related disorders in a Japanese Population. 2019/09
62.	Original article	Risk factors for hyponatremia after administration of hypotonic fluids 2019/08/30
63.	Original article	Clinical characteristics of Campylobacter enteritis after pediatric renal transplantation: A retrospective analysis from single cente 2019/04
64.	Original article	Molecular assay for an intronic variant in NUP93 that causes steroid resistant nephrotic syndrome. 2019/04
65.	Original article	Persistent Primary Cytomegalovirus Infection After Deceased Donor Kidney Transplant: Ganciclovir Susceptibility of Human Cytomegalovirus With UL97 D605E Mutation: A Case Report 2018/09
66.	Original article	Predominant but silent C1q deposits in mesangium on transplanted kidneys - long-term observational study 2018/03
67.	Original article	Amnionless-mediated glycosylation is crucial for cell surface targeting of cubilin in renal and intestinal cells. 2018/02
68.	Original article	Large abdominal protrusion. 2016/12
69.	Original article	Systemic lupus erythematosus presenting with mixed-type fulminant autoimmune hemolytic anemia 2016/06
70.	Original article	Systemic lupus erythematosus presenting with mixed-type fulminant autoimmune hemolytic anemia 2016/02
71.	Original article	Genetic, clinical, and pathologic backgrounds of patients with autosomal dominant Alport syndrome. 2016
72.	Original article	SIRPα interacts with nephrin at the podocyte slit diaphragm 2012/09
73.	Original article	V2 Vasopressin Receptor (V2R) Mutations in Partial Nephrogenic Diabetes Insipidus Highlight Protean Agonism of V2R Antagonists 2012/01
74.	Original article	Clinical features and mutational survey of NPHS2(podocin)in Japanese children with focal segmental glomerulosclerosis who underwent renal transplantation 2008/03
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■ Academic conference presentation

1.	Investigating the utility of serum NfL as a biomarker for macrocephalic type with subcortical cysts （Speech，General） 2025/06/05
2.	Prediction of 10-yr renal graft survival of deceased donors based on preoperative data using machine learning. （Poster notice，General） 2024/06/01
3.	Prediction of 10-yr renal graft survival of deceased donors based on preoperative data using machine learning. （Poster notice） 2024/04/25
4.	Two infantile patients with pseudohypoaldosteronism assoiated with congenital anomalies of the kidney and urinary tract （Poster notice，General） 2023/04/16
5.	En bloc kidney transplant from pediatric donors to teenage recipients: A single-center experience. （Speech，General） 2022/11/25
6.	Precise clinicopathologic findings for application of genetic testing in pediatric kidney transplant recipients with focal segmental glomerulosclerosis/steroid-resistant nephrotic syndrome. （Speech，General） 2022/10/07
7.	Cumulative dialysate glucose exposure is a risk factor for alterations of the peritoneum in PD using neutral-pH fluids （Speech，General） 2021/07/09
8.	A novel de novo truncating TRIM8 mutation associated with childhood-onset focal segmental glomerulosclerosis without epileptic encephalopathy （Poster notice，General） 2021/04/25
9.	Precise Clinicopathologic Findings may Increase the Detection Rate of Gene Mutations in Pediatric Kidney Transplant Recipients with Focal Segmental Glomerulosclerosis （Poster notice，General） 2019/11/08
10.	Lipoprotein apheresis for kidney disease in children in Japan （Speech，Panelist at Symposium/Workshop (Appointed)） 2019/10/20
11.	Introduction of PD in two children with profound intellectual and multiple disabilities （Poster notice，General） 2019/09/06
12.	Practice guidelines for pediatric PD in Japan （Speech，Panelist at Symposium/Workshop (Appointed)） 2019/09/06
13.	Clinical manifestations and genetic analysis of primary distal renal tubular acidosis （Poster notice，General） 2019/04/14
14.	The Size of Urinary Podocyte in Focal Segmental Glomerulosclerosis （Poster notice，General） 2018/10/27
15.	Clinicopathological Discrimination of Primary and Genetic Focal Segmental Glomerulosclerosis in Children （Poster notice，General） 2018/10/26
16.	Clinical and genetic analyses of primary distal renal tubular acidosis. （Speech，General） 2018/06/29
17.	The risk factors of hyponatremia during maintenance intravenous fluid therapy for children （Speech，General） 2018/06/09
18.	Clinical features of Campylobacter enteritis in pediatric kidney transplantation （Speech，General） 2018/04/22
19.	Clinical and genetic analysis of Joubert syndrome on renal replacement therapy （Speech，General） 2018/04/20
20.	Gastroenteritis by CMV reactivation after kidney transplantation （Poster notice，General） 2018/04/20
21.	ABO-incompatible living kidney transplantation with rituximab induction in children （Speech，General） 2018/02/24
22.	Cancer after pediatric kidney transplantation: a long-term single-center experience in Japan （Speech，General） 2018/02/24
23.	Hyperacute changes of podocytes in posttransplant recurrence of primary focal segmental glomerulosclerosis （Speech，General） 2018/02/24
24.	Infectious complications in pediatric kidney transplant recipients treated with rituximab: a single-center study （Speech，General） 2018/02/24
25.	Genital organ anomalies in female pediatric patients with congenital anomalies of the kidney and urinary tract. （Speech，General） 2017/10/07
26.	Mechanism of hyponatremia in Kawasaki disease: A role of nonosmotic ADH secretion and salt loss. （Speech，General） 2017/10/07
27.	Nation-wide survey of genetic disorders with low molecular weight proteinuria proposal of Japanese diagnostic criteria （Speech，General） 2017/06/02
28.	Outcom of pediatric ABO-incompatible living kidney transplantation with desensitization protocol based on plasmapheresis and rituximab: a single center experience. （Speech，General） 2017/05
29.	A case of congenital nephrotic syndrome with a heterozygous WT1 mutation complicated by bilateral multiple renal cysts mimicking polycystic kidney disease （Speech，General） 2017/04/08
30.	Long-term outcome of childhood-onset complicated nephrotic syndrome after multicenter, double-blind, randomized, placebo-controlled trial of rituximab （Speech，General） 2017/04/08
31.	Glycosylation defects of cubilin cause Imerslund-Gräsbeck syndrome. （Speech，General） 2016/11/18
32.	nfectious complications in pediatric kidney transplant recipients treated with rituximab: a single-center study. （Speech，General） 2016/11/18
33.	Proliferative glomerulonephritis with monoclonal IgG deposits in pediatric patients: a possible differential diagnosis of pediatric membranoploliferative glomerulonephritis. （Speech，General） 2016/11/18
34.	Risk factors for decline in eGFR below 60 ml/min/1.73m2 after kidney transplantation in Japanese children. （Speech，General） 2016/11/18
35.	Kidney transplantations with both recipients of kidneys from the same deceased donor with diabetic nephropathy. （Abstract Only，General） 2016/11
36.	Dent disease （Speech，General） 2016/09/24
37.	Genetics of RTA （Speech，General） 2016/09/23
38.	Risk factors for peritoneal dialysis failure in children. （Speech，General） 2016/09/23
39.	The cases of two recipients of kidneys from an identical deceased donor who had diabetic nephropathy. （Poster notice，General） 2016/07/16
40.	EPLIN (Epithelial Protein Lost in Neoplasm) Interacts with Paxillin and Regulates Mesangial Migration （Speech，General） 2012/11/03
41.	LMX1B Mutation with Residual Transcriptional Activity as a Cause of Nail-Patella-Like Renal Disease （Speech，General） 2012/11/03
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■ Education

1993/04～1999/03

Graduate School, Division of Medicine, The University of Tokyo, Graduated,

■ External Researcher ID

orcID

0000-0002-9483-8482