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平田 義弘
Department School of Medicine(Tokyo Women's Medical University Hospital), School of Medicine Position |
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| Article types | Case report |
| Language | English |
| Peer review | Non peer reviewed |
| Title | A case of acute liver failure caused by Budd-Chiari syndrome salvaged by brain-dead donor liver transplantation |
| Journal | Formal name：Clinical journal of gastroenterology Abbreviation：Clin J Gastroenterol ISSN code：18657265/18657265 |
| Domestic / Foregin | Foregin |
| Volume, Issue, Page | 17(1),pp.84-92 |
| Author and coauthor | KIMURA Kiwamu,OSAKI Akihiko,HIRATA Yoshihiro,EGAWA Hiroto,KOGISO Tomomi,NAKAMURA Gen,HASHIDATE Hideki,WAKABAYASHI Takuya,SATO Munehiro,WAGURI Nobuo |
| Publication date | 2024/02 |
| Summary | A 24-year-old man was admitted to our hospital with abdominal distension. He was found to have acute liver failure and diagnosed with Budd-Chiari syndrome based on angiography and liver biopsy. Liver transplantation was deemed necessary when angiography showed extensive thrombotic occlusion of the hepatic veins and liver biopsy revealed submassive hepatic necrosis. The patient was found to have the JAK2V617F mutation, indicating a myeloproliferative neoplasm as the background disease. He developed hepatic encephalopathy but remained conscious on on-line hemodiafiltration. Brain-dead donor liver transplantation was performed on hospital day 30. Since then, the patient has remained well. |
| DOI | 10.1007/s12328-023-01863-1 |
| PMID | 37773425 |