古田 晃久
   Department   School of Medicine(Tokyo Women's Medical University Hospital), School of Medicine
   Position   Assistant Professor
Article types Original article
Language English
Peer review Peer reviewed
Title Surgical repair of a truncus arteriosus with unilateral absence of the right proximal pulmonary artery.
Journal Formal name:Journal of cardiac surgery
Abbreviation:J Card Surg
ISSN code:08860440/15408191
Domestic / ForeginForegin
Publisher John Wiley & Sons, Inc.
Volume, Issue, Page 31(11),pp.703-705
Author and coauthor FURUTA Akihisa†, NAGASHIMA Mitsugi, HIRAMATSU Takeshi, MATSUMURA Goki, YAMAZAKI Kenji*
Authorship Lead author
Publication date 2016/11
Summary The unilateral absence of a proximal pulmonary artery (UAPPA) is rare and is most frequently accompanied by cardiovascular anomalies such as tetralogy of Fallot or septal defects. We report a patient with truncus arteriosus with UAPPA in which we performed a two-stage surgical repair. During the first palliative operation, a right modified Blalock-Taussig shunt was constructed to develop the hypoplastic right pulmonary artery. At 10 months, the patient underwent patch closure of a ventricular septal defect with integration of both pulmonary arteries, and reconstruction of the right ventricular outflow tract using a conduit. Four years postoperatively, he continues to do well.
DOI 10.1111/jocs.12848
PMID 27611449