フルイチ　ヨシヒロ   FURUICHI Yoshihiro   古市　好宏    所属   医学部 医学科（附属足立医療センター）    職種   准教授
論文種別	総説
言語種別	英語
査読の有無	査読あり
表題	Non-cirrhotic portal fibrosis/idiopathic portal hypertension: APASL recommendations for diagnosis and management.
掲載誌名	正式名：Hepatology international 略　 称：Hepatol Int ISSNコード：19360541/19360533
掲載区分	国外
巻・号・頁	54,pp.952-969
国際共著	国際共著
著者・共著者	Shukla Akash, Rockey Don C, Kamath Patrick S, Kleiner David E, Singh Ankita, Vaidya Arun, Koshy Abraham, Goel Ashish, Dökmeci A Kadir, Meena Babulal, Philips Cyriac Abby, Sharma Chhagan Bihari, Payawal Diana A, Kim Dong Joon, Lo Gin-Ho, Han Guohong, Qureshi Huma, Wanless Ian R, Jia Jidong, Sollano Jose D, Al Mahtab Mamun, Muthiah Mark Dhinesh, Sonderup Mark W, Nahum Mendez Sanchez, Merican Mohamed Ismail Bin, Ormeci Necati, Kawada Norifumi, Reddy Rajender, Dhiman R K, Gani Rino, Hameed Saeed S, Harindranath Sidharth, Jafri Wasim, Qi Xiaolong, Chawla Yogesh Kumar, Furuichi Yoshihiro, Zheng Ming-Hua, Sarin Shiv Kumar
発行年月	2024/11
概要	Since the Asian Pacific Association for the Study of the Liver (APASL) published guidelines on non-cirrhotic portal fibrosis/idiopathic portal hypertension in 2007, there has been a surge in new information, especially with the introduction of the term porto-sinusoidal vascular disorder (PSVD). Non-cirrhotic intra-hepatic causes of portal hypertension include disorders with a clearly identifiable etiology, such as schistosomiasis, as well as disorders with an unclear etiology such as non-cirrhotic portal fibrosis (NCPF), also termed idiopathic portal hypertension (IPH). This entity is being increasingly recognized as being associated with systemic disease and drug therapy, especially cancer therapy. An international working group with extensive expertise in portal hypertension was assigned with formulating consensus guidelines to clarify the definition, diagnosis, histological features, natural history, and management of NCPF/IPH, especially in the context of PSVD. The guidelines were prepared based on evidence from existing published literature. Whenever there was paucity of evidence, expert opinion was included after detailed deliberation. The goal of this manuscript, therefore, is to enhance the current understanding and help create global consensus on the issues surrounding NCPF/IPH.
DOI	10.1007/s12072-024-10739-6
PMID	39546143