コギソ トモミ   Kogiso Tomomi
  小木曽 智美
   所属   医学部 医学科(東京女子医科大学病院)
   職種   講師
論文種別 症例報告
言語種別 英語
査読の有無 査読なし
表題 A case of acute liver failure caused by Budd-Chiari syndrome salvaged by brain-dead donor liver transplantation
掲載誌名 正式名:Clinical journal of gastroenterology
略  称:Clin J Gastroenterol
ISSNコード:18657265/18657265
掲載区分国外
巻・号・頁 17(1),pp.84-92
著者・共著者 KIMURA Kiwamu,OSAKI Akihiko,HIRATA Yoshihiro,EGAWA Hiroto,KOGISO Tomomi,NAKAMURA Gen,HASHIDATE Hideki,WAKABAYASHI Takuya,SATO Munehiro,WAGURI Nobuo
発行年月 2024/02
概要 A 24-year-old man was admitted to our hospital with abdominal distension. He was found to have acute liver failure and diagnosed with Budd-Chiari syndrome based on angiography and liver biopsy. Liver transplantation was deemed necessary when angiography showed extensive thrombotic occlusion of the hepatic veins and liver biopsy revealed submassive hepatic necrosis. The patient was found to have the JAK2V617F mutation, indicating a myeloproliferative neoplasm as the background disease. He developed hepatic encephalopathy but remained conscious on on-line hemodiafiltration. Brain-dead donor liver transplantation was performed on hospital day 30. Since then, the patient has remained well.
DOI 10.1007/s12328-023-01863-1
PMID 37773425