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ホシノ ジユンイチ
Hoshino Jiyun'ichi
星野 純一 所属 医学部 医学科（東京女子医科大学病院） 職種 教授・基幹分野長 |
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| 論文種別 | 症例報告 |
| 言語種別 | 英語 |
| 査読の有無 | 査読なし |
| 表題 | 常染色体顕性尿細管間質性腎疾患サブタイプ肝細胞核因子1β患者における腎組織学的所見(Kidney Histology Findings in a Patient with Autosomal Dominant Tubulointerstitial Kidney Disease Subtype Hepatocyte Nuclear Factor 1β) |
| 掲載誌名 | 正式名：Internal Medicine 略 称：Intern Med ISSNコード：09182918/13497235 |
| 掲載区分 | 国外 |
| 出版社 | (一社)日本内科学会 |
| 巻・号・頁 | 62(3),pp.419-422 |
| 著者・共著者 | Nakayama Yuki, Sawa Naoki, Suwabe Tatsuya, Yamanouchi Masayuki, Ikuma Daisuke, Mizuno Hiroki, Hasegawa Eiko, Hoshino Junichi, Sekine Akinari, Oba Yuki, Kono Kei, Kinowaki Keiichi, Ohashi Kenichi, Yamaguchi Yutaka, Nozu Kandai, Ubara Yoshifumi |
| 発行年月 | 2023/02/01 |
| 概要 | We evaluated kidney histology in a 43-year-old woman with autosomal dominant tubulointerstitial kidney disease subtype hepatocyte nuclear factor 1β. Magnetic resonance imaging showed multiple cysts in the renal medullary area, and computed tomography showed hypoplasia of the pancreatic body and tail. A kidney biopsy showed thinning of the cortex, size reduction of glomerular tuft area, proximal tubule clustering, fibrosis around the tubules, loss of peritubular capillaries, and multilayered epithelial cells of cortical collecting ducts; this last finding was consistent with so-called medullary dysplasia specific to congenital disease, in which the renal pelvic epithelial cells enter the collecting duct. |
| DOI | 10.2169/internalmedicine.9364-22 |
| 文献番号 | 2024062445 |
| PMID | 35831109 |